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Polyglutamine aggregation nucleation: Thermodynamics of a highly unfavorable protein folding reaction

Polyglutamine (polyGln) aggregation is implicated in the disease progression of Huntington's disease and other expanded CAG repeat diseases. PolyGln aggregation in vitro follows a simple nucleated growth polymerization pathway without apparent complications such as populated intermediates, alte...

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Autors principals: Bhattacharyya, Anusri M., Thakur, Ashwani K., Wetzel, Ronald
Format: Article
Idioma:English
Publicat: National Academy of Sciences 2005
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC1266079/
https://ncbi.nlm.nih.gov/pubmed/16230628
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.0501651102
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