Out of breath: GM-CSFRα mutations disrupt surfactant homeostasis

Pulmonary alveolar proteinosis (PAP) is a rare disorder in which surfactant homeostasis in the lung is impaired, causing respiratory distress and, in severe cases, respiratory failure. Most cases of PAP are associated with the formation of autoantibodies against the cytokine granulocyte/macrophage c...

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Autori principali: Notarangelo, Luigi D., Pessach, Itai
Natura: Articolo
Lingua:English
Pubblicazione: The Rockefeller University Press 2008
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Commentaries
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2585835/
https://ncbi.nlm.nih.gov/pubmed/19015311
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1084/jem.20082378
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Accesso online

https://ncbi.nlm.nih.gov/pmc/articles/PMC2585835/
https://ncbi.nlm.nih.gov/pubmed/19015311
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1084/jem.20082378

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