Bibliotecas PUC-SP - Busca Integrada

Ivacaftor treatment of cystic fibrosis patients with the G551D mutation: a review of the evidence

بواسطة Kavitha Kotha, John P. Clancy
الحاوية / القاعدة Therapeutic Advances in Respiratory Disease (2013-10-01)

Flexible semiparametric joint modeling: an application to estimate individual lung function decline and risk of pulmonary exacerbations in cystic fibrosis

بواسطة Dan Li, Ruth Keogh, John P. Clancy, Rhonda D. Szczesniak
الحاوية / القاعدة Emerging Themes in Epidemiology (2017-11-01)

An Animated Functional Data Analysis Interface to Cluster Rapid Lung Function Decline and Enhance Center-Level Care in Cystic Fibrosis

بواسطة Jesse Pratt, Weiji Su, Don Hayes, John P. Clancy, Rhonda D. Szczesniak
منشور في 2021-01-01

CFTR dysfunction in smooth muscle drives TGFβ dependent airway hyperreactivity

بواسطة Elizabeth L. Kramer, Kristin M. Hudock, Cynthia R. Davidson, John P. Clancy
الحاوية / القاعدة Respiratory Research (2023-08-01)

2045 The role of TGFβ in driving early cystic fibrosis lung disease

بواسطة Elizabeth L. Kramer, William Hardie, Kristin Hudock, Cynthia Davidson, Alicia Ostmann, John P. Clancy
الحاوية / القاعدة Journal of Clinical and Translational Science (2018-06-01)

Improving Detection of Rapid Cystic Fibrosis Disease Progression–Early Translation of a Predictive Algorithm Into a Point-of-Care Tool

بواسطة Rhonda D. Szczesniak, Cole Brokamp, Weiji Su, Gary L. Mcphail, John Pestian, John P. Clancy
الحاوية / القاعدة IEEE Journal of Translational Engineering in Health and Medicine (2019-01-01)

Phenotypic Alteration of an Established Human Airway Cell Line by Media Selection

بواسطة Galit Livnat, Jessica D. Meeker, Alicia J. Ostmann, Lauren M. Strecker, John P. Clancy, John J. Brewington
الحاوية / القاعدة International Journal of Molecular Sciences (2023-01-01)

3123 TGFbeta, Early Cytokine Dysregulation, and Airway Smooth Muscle Dysfunction in Cystic Fibrosis

بواسطة Elizabeth L Kramer, Rhonda Szczesniak, Weiji Su, Satish Madala, Kristin Hudock, Cynthia Davidson, Alicia Ostmann, Lauren Strecker, John P. Clancy
الحاوية / القاعدة Journal of Clinical and Translational Science (2019-03-01)

Data driven decision making to characterize clinical personas of parents of children with cystic fibrosis: a mixed methods study

بواسطة Rhonda D. Szczesniak, Teresa Pestian, Leo L. Duan, Dan Li, Sophia Stamper, Brycen Ferrara, Elizabeth Kramer, John P. Clancy, Daniel Grossoehme
الحاوية / القاعدة BMC Pulmonary Medicine (2020-06-01)

Tgf-beta downregulation of distinct chloride channels in cystic fibrosis-affected epithelia.

بواسطة Hongtao Sun, William T Harris, Stephanie Kortyka, Kavitha Kotha, Alicia J Ostmann, Amir Rezayat, Anusha Sridharan, Yan Sanders, Anjaparavanda P Naren, John P Clancy
الحاوية / القاعدة PLoS ONE (2014-01-01)

Elexacaftor/tezacaftor/ivacaftor’s effects on cystic fibrosis infections are maintained, but not increased, after 3.5 years of treatment

بواسطة Sarah J. Morgan, Ellis Coulter, Hannah L. Betts, George M. Solomon, John P. Clancy, Steven M. Rowe, David P. Nichols, Pradeep K. Singh, the PROMISE-Micro Study Group
الحاوية / القاعدة The Journal of Clinical Investigation (2024-10-01)

Seasonality, mediation and comparison (SMAC) methods to identify influences on lung function decline

بواسطة Emrah Gecili, Anushka Palipana, Cole Brokamp, Rui Huang, Eleni-Rosalina Andrinopoulou, Teresa Pestian, Erika Rasnick, Ruth H. Keogh, Yizhao Ni, John P. Clancy, Patrick Ryan, Rhonda D. Szczesniak
الحاوية / القاعدة MethodsX (2021-01-01)

Optimizing nasal potential difference analysis for CFTR modulator development: assessment of ivacaftor in CF subjects with the G551D-CFTR mutation.

بواسطة Steven M Rowe, Bo Liu, Aubrey Hill, Heather Hathorne, Morty Cohen, John R Beamer, Frank J Accurso, Qunming Dong, Claudia L Ordoñez, Anne J Stone, Eric R Olson, John P Clancy, VX06-770-101 Study Group
الحاوية / القاعدة PLoS ONE (2013-01-01)

Social-environmental phenotypes of rapid cystic fibrosis lung disease progression in adolescents and young adults living in the United States

بواسطة Anushka K. Palipana, Andrew Vancil, Emrah Gecili, Erika Rasnick, Daniel Ehrlich, Teresa Pestian, Eleni-Rosalina Andrinopoulou, Pedro M. Afonso, Ruth H. Keogh, Yizhao Ni, Judith W. Dexheimer, John P. Clancy, Patrick Ryan, Cole Brokamp, Rhonda D. Szczesniak
الحاوية / القاعدة Environmental Advances (2023-12-01)

Pharmacologic improvement of CFTR function rapidly decreases sputum pathogen density, but lung infections generally persist

بواسطة David P. Nichols, Sarah J. Morgan, Michelle Skalland, Anh T. Vo, Jill M. Van Dalfsen, Sachinkumar B.P. Singh, Wendy Ni, Lucas R. Hoffman, Kailee McGeer, Sonya L. Heltshe, John P. Clancy, Steven M. Rowe, Peter Jorth, Pradeep K. Singh, the PROMISE-Micro Study Group
الحاوية / القاعدة The Journal of Clinical Investigation (2023-05-01)

Multicenter intestinal current measurements in rectal biopsies from CF and non-CF subjects to monitor CFTR function.

بواسطة John P Clancy, Rhonda D Szczesniak, Melissa A Ashlock, Sarah E Ernst, Lijuan Fan, Douglas B Hornick, Philip H Karp, Umer Khan, James Lymp, Alicia J Ostmann, Amir Rezayat, Timothy D Starner, Shajan P Sugandha, Hongtao Sun, Nancy Quinney, Scott H Donaldson, Steven M Rowe, Sherif E Gabriel
الحاوية / القاعدة PLoS ONE (2013-01-01)

Prospective multicenter randomized patient recruitment and sample collection to enable future measurements of sputum biomarkers of inflammation in an observational study of cystic...

بواسطة Theodore G. Liou, Frederick R. Adler, Natalia Argel, Fadi Asfour, Perry S. Brown, Barbara A. Chatfield, Cori L. Daines, Dixie Durham, Jessica A. Francis, Barbara Glover, Theresa Heynekamp, John R. Hoidal, Judy L. Jensen, Ruth Keogh, Carol M. Kopecky, Noah Lechtzin, Yanping Li, Jerimiah Lysinger, Osmara Molina, Craig Nakamura, Kristyn A. Packer, Katie R. Poch, Alexandra L. Quittner, Peggy Radford, Abby J. Redway, Scott D. Sagel, Shawna Sprandel, Jennifer L. Taylor-Cousar, Jane B. Vroom, Ryan Yoshikawa, John P. Clancy, J. Stuart Elborn, Kenneth N. Olivier, David R. Cox
الحاوية / القاعدة BMC Medical Research Methodology (2019-04-01)

Airway inflammation accelerates pulmonary exacerbations in cystic fibrosis

بواسطة Theodore G. Liou, Natalia Argel, Fadi Asfour, Perry S. Brown, Barbara A. Chatfield, David R. Cox, Cori L. Daines, Dixie Durham, Jessica A. Francis, Barbara Glover, My Helms, Theresa Heynekamp, John R. Hoidal, Judy L. Jensen, Christiana Kartsonaki, Ruth Keogh, Carol M. Kopecky, Noah Lechtzin, Yanping Li, Jerimiah Lysinger, Osmara Molina, Craig Nakamura, Kristyn A. Packer, Robert Paine, III, Katie R. Poch, Alexandra L. Quittner, Peggy Radford, Abby J. Redway, Scott D. Sagel, Rhonda D. Szczesniak, Shawna Sprandel, Jennifer L. Taylor-Cousar, Jane B. Vroom, Ryan Yoshikawa, John P. Clancy, J. Stuart Elborn, Kenneth N. Olivier, Frederick R. Adler
الحاوية / القاعدة iScience (2024-03-01)