Bibliotecas PUC-SP - Busca Integrada

Lymphangioleiomyomatosis in patients with tuberous sclerosis: a national centre audit

Por Jan Johnson, Wendy Somerfield, Simon R. Johnson
Publicado no Orphanet Journal of Rare Diseases (2024-03-01)

Wild type mesenchymal cells contribute to the lung pathology of lymphangioleiomyomatosis.

Por Debbie Clements, Arundhati Dongre, Vera P Krymskaya, Simon R Johnson
Publicado no PLoS ONE (2015-01-01)

Extra-cellular matrix proteins induce matrix metalloproteinase-1 (MMP-1) activity and increase airway smooth muscle contraction in asthma.

Por Natasha K Rogers, Debbie Clements, Arundhati Dongre, Tim W Harrison, Dominic Shaw, Simon R Johnson
Publicado no PLoS ONE (2014-01-01)

Evolution of lung pathology in lymphangioleiomyomatosis: associations with disease course and treatment response

Por Suzanne Miller, Iain D Stewart, Debbie Clements, Irshad Soomro, Roya Babaei‐Jadidi, Simon R Johnson
Publicado no The Journal of Pathology: Clinical Research (2020-07-01)

Elevated PLAUR is observed in the airway epithelium of asthma patients and blocking improves barrier integrity

Por Michael A. Portelli, Sangita Bhaker, Vincent Pang, David O. Bates, Simon R. Johnson, Andrew P. Mazar, Dominick Shaw, Christopher Brightling, Ian Sayers
Publicado no Clinical and Translational Allergy (2023-10-01)

Air travel and incidence of pneumothorax in lymphangioleiomyomatosis

Por Cynthia Gonano, Jérôme Pasquier, Cécile Daccord, Simon R. Johnson, Sergio Harari, Violette Leclerc, Lucy Falconer, Eleonora Miano, Jean-François Cordier, Vincent Cottin, Romain Lazor
Publicado no Orphanet Journal of Rare Diseases (2018-12-01)

Accelerated 19F·MRI Detection of Matrix Metalloproteinase-2/-9 through Responsive Deactivation of Paramagnetic Relaxation Enhancement

Por Henryk M. Faas, James L. Krupa, Alexander J. Taylor, Francesco Zamberlan, Christopher J. Philp, Huw E. L. Williams, Simon R. Johnson, Galina E. Pavlovskaya, Neil R. Thomas, Thomas Meersmann
Publicado em 2019-01-01

mTOR dysregulation induces IL-6 and paracrine AT2 cell senescence impeding lung repair in lymphangioleiomyomatosis

Por Roya Babaei-Jadidi, Debbie Clements, Yixin Wu, Ken Chen, Suzanne Miller, Manuela Platé, Kyungtae Lim, Ryan Rue, Vera P. Krymskaya, Rachel Chambers, Emma L. Rawlins, Yan Xu, Simon R. Johnson
Publicado no Nature Communications (2025-10-01)

The role of inflammation resolution speed in airway smooth muscle mass accumulation in asthma: insight from a theoretical model.

Por Igor L Chernyavsky, Huguette Croisier, Lloyd A C Chapman, Laura S Kimpton, Jonathan E Hiorns, Bindi S Brook, Oliver E Jensen, Charlotte K Billington, Ian P Hall, Simon R Johnson
Publicado no PLoS ONE (2014-01-01)

Tuberous Sclerosis Complex (TSC): Expert Recommendations for Provision of Coordinated Care

Por Nicholas M. P. Annear, Nicholas M. P. Annear, Richard E. Appleton, Zahabiyah Bassi, Rupesh Bhatt, Patrick F. Bolton, Pamela Crawford, Alex Crowe, Maureen Tossi, Maureen Tossi, Frances Elmslie, Frances Elmslie, Eric Finlay, Daniel P. Gale, Alex Henderson, Elizabeth A. Jones, Elizabeth A. Jones, Simon R. Johnson, Simon R. Johnson, Shelagh Joss, Larissa Kerecuk, Graham Lipkin, Patrick J. Morrison, Finbar J. O'Callaghan, Jill Cadwgan, Jill Cadwgan, Jill Cadwgan, Albert C. M. Ong, Albert C. M. Ong, Julian R. Sampson, Charles Shepherd, J. Chris Kingswood, J. Chris Kingswood, J. Chris Kingswood
Publicado no Frontiers in Neurology (2019-11-01)

A lung targeted miR-29 mimic as a therapy for pulmonary fibrosis

Por Maurizio Chioccioli, Subhadeep Roy, Rachel Newell, Linda Pestano, Brent Dickinson, Kevin Rigby, Jose Herazo-Maya, Gisli Jenkins, Steward Ian, Gauri Saini, Simon R. Johnson, Rebecca Braybrooke, Guying Yu, Maor Sauler, Farida Ahangari, Shuizi Ding, Joseph DeIuliis, Nachelle Aurelien, Rusty L. Montgomery, Naftali Kaminski
Publicado no EBioMedicine (2022-11-01)

mTOR pathway diseases: challenges and opportunities from bench to bedside and the mTOR node

Por Laura Mantoan Ritter, Nicholas M. P. Annear, Emma L. Baple, Leila Y. Ben-Chaabane, Istvan Bodi, Lauren Brosson, Jill E. Cadwgan, Bryn Coslett, Andrew H. Crosby, D. Mark Davies, Nicola Daykin, Stefanie Dedeurwaerdere, Christina Dühring Fenger, Elaine A. Dunlop, Frances V. Elmslie, Marie Girodengo, Sophie Hambleton, Anna C. Jansen, Simon R. Johnson, Kelly C. Kearley, John C. Kingswood, Liisi Laaniste, Katherine Lachlan, Andrew Latchford, Ralitsa R. Madsen, Sahar Mansour, Simeon R. Mihaylov, Louwai Muhammed, Claire Oliver, Tom Pepper, Lettie E. Rawlins, Ina Schim van der Loeff, Ata Siddiqui, Pooja Takhar, Katrina Tatton-Brown, Andrew R. Tee, Priyanka Tibarewal, Charlotte Tye, Sila K. Ultanir, Bart Vanhaesebroeck, Benjamin Zare, Deb K. Pal, Joseph M. Bateman
Publicado no Orphanet Journal of Rare Diseases (2025-05-01)

Histamine signaling and metabolism identify potential biomarkers and therapies for lymphangioleiomyomatosis

Por Carmen Herranz, Francesca Mateo, Alexandra Baiges, Gorka Ruiz de Garibay, Alexandra Junza, Simon R Johnson, Suzanne Miller, Nadia García, Jordi Capellades, Antonio Gómez, August Vidal, Luis Palomero, Roderic Espín, Ana I Extremera, Eline Blommaert, Eva Revilla‐López, Berta Saez, Susana Gómez‐Ollés, Julio Ancochea, Claudia Valenzuela, Tamara Alonso, Piedad Ussetti, Rosalía Laporta, Antoni Xaubet, José A Rodríguez‐Portal, Ana Montes‐Worboys, Carlos Machahua, Jaume Bordas, Javier A Menendez, Josep M Cruzado, Roser Guiteras, Christophe Bontoux, Concettina La Motta, Aleix Noguera‐Castells, Mario Mancino, Enrique Lastra, Raúl Rigo‐Bonnin, Jose C Perales, Francesc Viñals, Alvaro Lahiguera, Xiaohu Zhang, Daniel Cuadras, Coline H M van Moorsel, Joanne J van der Vis, Marian J R Quanjel, Harilaos Filippakis, Razq Hakem, Chiara Gorrini, Marc Ferrer, Aslihan Ugun‐Klusek, Ellen Billett, Elżbieta Radzikowska, Álvaro Casanova, María Molina‐Molina, Antonio Roman, Oscar Yanes, Miquel A Pujana
Publicado no EMBO Molecular Medicine (2021-08-01)

Understanding the burden of interstitial lung disease post-COVID-19: the UK Interstitial Lung Disease-Long COVID Study (UKILD-Long COVID)

Por R Gisli Jenkins, A John Simpson, Jennifer K Quint, Nicholas D Weatherley, Guilhem Collier, Jim M Wild, David R Thickett, Shaney L Barratt, Puja Mehta, Nazia Chaudhuri, Ling-Pei Ho, Lisa G Spencer, John F Blaikley, Fasihul Khan, Iain Stewart, John Kenneth Baillie, Rod Lawson, Simon R Johnson, Paul Beirne, Mark Spears, Laura Fabbri, Joseph Jacob, Fergus V Gleeson, Mark G Jones, Bibek Gooptu, Rachel C Chambers, Philip L Molyneaux, Peter M George, Michael A Gibbons, Emma K Denneny, Melissa Heightman, Toby E Hillman, Joanna C Porter, Manuela Platé, Stephen M Bianchi, Chris E Brightling, Richard James Allen, Annemarie Docherty, Jane A Mitchell, Ian P Hall, Jonathan Brooke, Louise V Wain, Malcolm Semple, Raminder Aul, Neil A Hanley, Krisnah Poinasamy, Pilar Rivera-Ortega, DJF Smith, Stefan C Stanel, A A Roger Thompson, Simon LF Walsh, Mark Everard Weeks, Dan G Wootton, Karen Piper Hanley
Publicado no BMJ Open Respiratory Research (2021-11-01)