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Farber's disease (lysosomal acid ceramidase deficiency).

The patient presented with progressive joint deformity, a hoarse voice, subsequent cachexia, and myoclonic seizures. She was first seen aged 22 months and died aged 6 years. A diagnosis of Farber's disease was made by demonstrating a deficiency of acid ceramidase both in leucocytes and fibrobla...

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Detalhes bibliográficos
Main Authors: Jameson, R A, Holt, P J, Keen, J H
Formato: Artigo
Idioma:English
Publicado em: 1987
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC1002193/
https://ncbi.nlm.nih.gov/pubmed/3662645
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