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Immunochemical studies on cultured fibroblasts from patients with homocystinuria due to cystathionine beta-synthase deficiency.

Fibroblast extracts from 20 individuals with homocystinuria due to cystathionine beta-synthase deficiency were analyzed for the presence of immunoreactive synthase antigen as cross-reacting material (CRM). CRM was quantitated by competitive and direct immunotitration using rabbit antiserum against h...

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Detalhes bibliográficos
Main Authors: Skovby, F, Kraus, J, Redlich, C, Rosenberg, L E
Formato: Artigo
Idioma:English
Publicado em: 1982
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC1685209/
https://ncbi.nlm.nih.gov/pubmed/7081217
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