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Acquired C1 inhibitor (C1-INH) deficiency type II. Replacement therapy with C1-INH and analysis of patients' C1-INH and anti-C1-INH autoantibodies.

The response of two patients with autoantibody-mediated C1-inhibitor (C1-INH) deficiency to replacement therapy with C1-INH was studied over a period of 3 d. In patient 1 an acute attack of angioedema was successfully managed by infusion of 1,000 U of C1-INH concentrate. C1-INH function returned to...

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Main Authors: Alsenz, J, Lambris, J D, Bork, K, Loos, M, Goldhaber, J I, Ji, S, Lamp, S T, Weiss, J N, Bern, M J, Sturbaum, C W, Karayalcin, S S, Berschneider, H M, Wachsman, J T, Powell, D W, Huot, R I, Armstrong, D L, Chanh, T C, Peters, M G, Secrist, H, Anders, K R, Nash, G S, Rich, S R, MacDermott, R P, Sekiya, K, Ghatei, M A, Salahuddin, M J, Bishop, A E, Hamid, Q A, Ibayashi, H, Polak, J M, Bloom, S R, Laurence, J, Friedman, S M, Chartash, E K, Crow, M K, Posnett, D N, Abman, S H, Shanley, P F, Accurso, F J, Preisig, P A, Alpern, R J, Melby, P C, Neva, F A, Sacks, D L, Morris, A C, Hagler, H K, Willerson, J T, Buja, L M, Ariga, T, Igarashi, T, Ramesh, N, Parad, R, Cicardi, M, Davis, A E, Storch, G A, Park, C S, Dohner, D E, Merke, J, Milde, P, Lewicka, S, Hügel, U, Klaus, G, Mangelsdorf, D J, Haussler, M R, Rauterberg, E W, Ritz, E, Kazura, J W, Wenger, J D, Salata, R A, Budzynski, A Z, Goldsmith, G H, Cooper, S C, Roncari, D A, Hughes, D E, MacDonald, B R, Russell, R G, Gowen, M, Maridonneau-Parini, I, Errasfa, M, Russo-Marie, F, Ellison, K E, Ingelfinger, J R, Pivor, M, Dzau, V J, Gordon, J B, Ganz, P, Nabel, E G, Fish, R D, Zebede, J, Mudge, G H, Alexander, R W, Selwyn, A P, Donowitz, M, Cohen, M E, Gould, M, Sharp, G W, Perez, H D, Elfman, F, Marder, S, Lobo, E, Ives, H E, Pui, C H, Raskind, W H, Kitchingman, G R, Raimondi, S C, Behm, F G, Murphy, S B, Crist, W M, Fialkow, P J, Williams, D L, Arai, M, Scandella, D, Hoyer, L W, Liebhaber, S A, Urbanek, M, Ray, J, Tuan, R S, Cooke, N E, Albelda, S M, Daise, M, Levine, E M, Buck, C A, Ray, R, Snyder, R C, Thomas, S, Koller, C A, Miller, D M, Smith, C W, Marlin, S D, Rothlein, R, Toman, C, Anderson, D C, Yen, F T, Deckelbaum, R J, Mann, C J, Marcel, Y L, Milne, R W, Tall, A R, Cartwright, C A, Kamps, M P, Meisler, A I, Pipas, J M, Eckhart, W, Arnold, A, Kim, H G, Gaz, R D, Eddy, R L, Fukushima, Y, Byers, M G, Shows, T B, Kronenberg, H M, Cheung, A L, Fischetti, V A, Lynch, C J, Blackmore, P F, Johnson, E H, Wange, R L, Krone, P K, Exton, J H, Toyofuku, T, Koyama, S, Kobayashi, T, Kusama, S, Ueda, G, Bouhassira, E E, Lachman, H, Krishnamoorthy, R, Labie, D, Nagel, R L, Levy, D, Kost, J, Meshulam, Y, Langer, R, Paradisi, R, Frank, G, Grossi, G, Venturoli, S, Porcu, E, Capelli, M, Galassi, E, Flamigni, C, Shaw, K J, Do, Y S, Kjos, S, Anderson, P W, Shinagawa, T, Dubeau, L, Hsueh, W A, Barsony, J, McKoy, W, DeGrange, D A, Liberman, U A, Marx, S J, Pecha, B, Low, D, O'Hanley, P, Packer, D L, Grant, A O, Strauss, H C, Starmer, C F, Miller, Y E, Minna, J D, Gazdar, A F, Mahley, R W, Weisgraber, K H, Hussain, M M, Greenman, B, Fisher, M, Vogel, T, Gorecki, M, Tan, E M, Holguin, M H, Fredrick, L R, Bernshaw, N J, Wilcox, L A, Parker, C J, Eidt, J F, Allison, P, Noble, S, Ashton, J, Golino, P, McNatt, J, Gustafson, E J, Schmaier, A H, Wachtfogel, Y T, Kaufman, N, Kucich, U, Colman, R W, Deitch, E A, Ma, L, Ma, W J, Grisham, M B, Granger, D N, Specian, R D, Berg, R D, Chackal-Roy, M, Niemeyer, C, Moore, M, Zetter, B R, Kawa-Ha, K, Ishihara, S, Ninomiya, T, Yumura-Yagi, K, Hara, J, Murayama, F, Tawa, A, Hirai, K
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Publicado em: 1989
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC303898/
https://ncbi.nlm.nih.gov/pubmed/2723058
https://ncbi.nlm.nih.gov/pmc/articles/PMC303899/
https://ncbi.nlm.nih.gov/pubmed/2723059
https://ncbi.nlm.nih.gov/pmc/articles/PMC303900/
https://ncbi.nlm.nih.gov/pubmed/2723060
https://ncbi.nlm.nih.gov/pmc/articles/PMC303901/
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https://ncbi.nlm.nih.gov/pmc/articles/PMC303902/
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https://ncbi.nlm.nih.gov/pmc/articles/PMC303903/
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https://ncbi.nlm.nih.gov/pmc/articles/PMC303905/
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https://ncbi.nlm.nih.gov/pmc/articles/PMC303931/
https://ncbi.nlm.nih.gov/pubmed/2542380
https://ncbi.nlm.nih.gov/pmc/articles/PMC303932/
https://ncbi.nlm.nih.gov/pubmed/2723072
https://ncbi.nlm.nih.gov/pmc/articles/PMC303933/
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https://ncbi.nlm.nih.gov/pmc/articles/PMC303934/
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https://ncbi.nlm.nih.gov/pmc/articles/PMC303935/
https://ncbi.nlm.nih.gov/pubmed/2656762
https://ncbi.nlm.nih.gov/pmc/articles/PMC303936/
https://ncbi.nlm.nih.gov/pubmed/2542381
https://ncbi.nlm.nih.gov/pmc/articles/PMC303937/
https://ncbi.nlm.nih.gov/pubmed/2566625
https://ncbi.nlm.nih.gov/pmc/articles/PMC303938/
https://ncbi.nlm.nih.gov/pubmed/2542382
https://ncbi.nlm.nih.gov/pmc/articles/PMC303939/
https://ncbi.nlm.nih.gov/pubmed/2542383
https://ncbi.nlm.nih.gov/pmc/articles/PMC303940/
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https://ncbi.nlm.nih.gov/pmc/articles/PMC303945/
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https://ncbi.nlm.nih.gov/pmc/articles/PMC303946/
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https://ncbi.nlm.nih.gov/pmc/articles/PMC303947/
https://ncbi.nlm.nih.gov/pubmed/2661588
https://ncbi.nlm.nih.gov/pmc/articles/PMC303948/
https://ncbi.nlm.nih.gov/pubmed/2738152
https://ncbi.nlm.nih.gov/pmc/articles/PMC303949/
https://ncbi.nlm.nih.gov/pubmed/2661590
https://ncbi.nlm.nih.gov/pmc/articles/PMC303950/
https://ncbi.nlm.nih.gov/pubmed/2786890
https://ncbi.nlm.nih.gov/pmc/articles/PMC303951/
https://ncbi.nlm.nih.gov/pubmed/2544630
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https://ncbi.nlm.nih.gov/pmc/articles/PMC303898/
https://ncbi.nlm.nih.gov/pubmed/2723058
https://ncbi.nlm.nih.gov/pmc/articles/PMC303899/
https://ncbi.nlm.nih.gov/pubmed/2723059
https://ncbi.nlm.nih.gov/pmc/articles/PMC303900/
https://ncbi.nlm.nih.gov/pubmed/2723060
https://ncbi.nlm.nih.gov/pmc/articles/PMC303901/
https://ncbi.nlm.nih.gov/pubmed/2542373
https://ncbi.nlm.nih.gov/pmc/articles/PMC303902/
https://ncbi.nlm.nih.gov/pubmed/2498391
https://ncbi.nlm.nih.gov/pmc/articles/PMC303903/
https://ncbi.nlm.nih.gov/pubmed/2723061
https://ncbi.nlm.nih.gov/pmc/articles/PMC303904/
https://ncbi.nlm.nih.gov/pubmed/2470786
https://ncbi.nlm.nih.gov/pmc/articles/PMC303905/
https://ncbi.nlm.nih.gov/pubmed/2723062
https://ncbi.nlm.nih.gov/pmc/articles/PMC303906/
https://ncbi.nlm.nih.gov/pubmed/2542374
https://ncbi.nlm.nih.gov/pmc/articles/PMC303907/
https://ncbi.nlm.nih.gov/pubmed/2470787
https://ncbi.nlm.nih.gov/pmc/articles/PMC303908/
https://ncbi.nlm.nih.gov/pubmed/2542375
https://ncbi.nlm.nih.gov/pmc/articles/PMC303909/
https://ncbi.nlm.nih.gov/pubmed/2723063
https://ncbi.nlm.nih.gov/pmc/articles/PMC303910/
https://ncbi.nlm.nih.gov/pubmed/2723064
https://ncbi.nlm.nih.gov/pmc/articles/PMC303911/
https://ncbi.nlm.nih.gov/pubmed/2542376
https://ncbi.nlm.nih.gov/pmc/articles/PMC303912/
https://ncbi.nlm.nih.gov/pubmed/2542377
https://ncbi.nlm.nih.gov/pmc/articles/PMC303913/
https://ncbi.nlm.nih.gov/pubmed/2723065
https://ncbi.nlm.nih.gov/pmc/articles/PMC303914/
https://ncbi.nlm.nih.gov/pubmed/2524504
https://ncbi.nlm.nih.gov/pmc/articles/PMC303915/
https://ncbi.nlm.nih.gov/pubmed/2542378
https://ncbi.nlm.nih.gov/pmc/articles/PMC303916/
https://ncbi.nlm.nih.gov/pubmed/2723066
https://ncbi.nlm.nih.gov/pmc/articles/PMC303917/
https://ncbi.nlm.nih.gov/pubmed/2723067
https://ncbi.nlm.nih.gov/pmc/articles/PMC303918/
https://ncbi.nlm.nih.gov/pubmed/2498392
https://ncbi.nlm.nih.gov/pmc/articles/PMC303919/
https://ncbi.nlm.nih.gov/pubmed/2723068
https://ncbi.nlm.nih.gov/pmc/articles/PMC303920/
https://ncbi.nlm.nih.gov/pubmed/2566623
https://ncbi.nlm.nih.gov/pmc/articles/PMC303921/
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https://ncbi.nlm.nih.gov/pmc/articles/PMC303922/
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https://ncbi.nlm.nih.gov/pmc/articles/PMC303923/
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https://ncbi.nlm.nih.gov/pmc/articles/PMC303924/
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https://ncbi.nlm.nih.gov/pmc/articles/PMC303925/
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https://ncbi.nlm.nih.gov/pubmed/2656761
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https://ncbi.nlm.nih.gov/pubmed/2498395
https://ncbi.nlm.nih.gov/pmc/articles/PMC303931/
https://ncbi.nlm.nih.gov/pubmed/2542380
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https://ncbi.nlm.nih.gov/pubmed/2723072
https://ncbi.nlm.nih.gov/pmc/articles/PMC303933/
https://ncbi.nlm.nih.gov/pubmed/2498396
https://ncbi.nlm.nih.gov/pmc/articles/PMC303934/
https://ncbi.nlm.nih.gov/pubmed/2723073
https://ncbi.nlm.nih.gov/pmc/articles/PMC303935/
https://ncbi.nlm.nih.gov/pubmed/2656762
https://ncbi.nlm.nih.gov/pmc/articles/PMC303936/
https://ncbi.nlm.nih.gov/pubmed/2542381
https://ncbi.nlm.nih.gov/pmc/articles/PMC303937/
https://ncbi.nlm.nih.gov/pubmed/2566625
https://ncbi.nlm.nih.gov/pmc/articles/PMC303938/
https://ncbi.nlm.nih.gov/pubmed/2542382
https://ncbi.nlm.nih.gov/pmc/articles/PMC303939/
https://ncbi.nlm.nih.gov/pubmed/2542383
https://ncbi.nlm.nih.gov/pmc/articles/PMC303940/
https://ncbi.nlm.nih.gov/pubmed/2723074
https://ncbi.nlm.nih.gov/pmc/articles/PMC303945/
https://ncbi.nlm.nih.gov/pubmed/2472423
https://ncbi.nlm.nih.gov/pmc/articles/PMC303946/
https://ncbi.nlm.nih.gov/pubmed/2738160
https://ncbi.nlm.nih.gov/pmc/articles/PMC303947/
https://ncbi.nlm.nih.gov/pubmed/2661588
https://ncbi.nlm.nih.gov/pmc/articles/PMC303948/
https://ncbi.nlm.nih.gov/pubmed/2738152
https://ncbi.nlm.nih.gov/pmc/articles/PMC303949/
https://ncbi.nlm.nih.gov/pubmed/2661590
https://ncbi.nlm.nih.gov/pmc/articles/PMC303950/
https://ncbi.nlm.nih.gov/pubmed/2786890
https://ncbi.nlm.nih.gov/pmc/articles/PMC303951/
https://ncbi.nlm.nih.gov/pubmed/2544630