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Paraneoplastic Pemphigus: A Paraneoplastic Autoimmune Multiorgan Syndrome or Autoimmune Multiorganopathy?

Paraneoplastic pemphigus (PNP), a clinically and immunopathologically distinct mucocutaneous blistering dermatosis, is a severe form of autoimmune multiorgan syndrome generally associated with poor therapeutic outcome and high mortality. This IgG-mediated disease is initiated by an obvious or occult...

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Detalhes bibliográficos
Formato: Artigo
Idioma:en
Publicado em: Hindawi Publishing Corporation 2012
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3535815/
https://ncbi.nlm.nih.gov/pubmed/23316398
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2012/207126
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